Congenital biliary atresia is one of the most common malformations in hepatobiliary congenital diseases, with a higher incidence in China compared to the West, and more prevalent in females than males, approximately 1.5:1. The disease cause of congenital biliary atresia remains unclear and is clinically classified into correctable and non-correctable types. The former shows good outcomes with timely treatment, while the latter has poorer results.

bubble_chart Clinical Manifestations

1. Progressive jaundice worsens, stool color turns clay-colored, and urine color darkens to tea-red;
2. abdominal distension and fullness, hepatomegaly, ascites.

bubble_chart Diagnosis

1. Progressive jaundice worsens, stool color changes to clay-colored, and urine color deepens to tea-colored;
2. abdominal distension and fullness, hepatomegaly, ascites;
3. abnormal liver function;
4. B-ultrasound indicates biliary atresia;
5. CT shows biliary atresia.

bubble_chart Treatment Measures

1. Correctable type: Perform Roux-en-Y cholangiojejunostomy;
2. Non-correctable type: Perform Kasai procedure or liver transplantation.

bubble_chart Cure Criteria

1. Cure: Jaundice subsides, stool normalizes, liver function returns to normal, biliary tract can recover to normal;
2. Improvement: Jaundice alleviates, stool basically normalizes, liver function mostly normalizes, liver does not continue to enlarge;
3. No cure: No change.